From: The complete European guidelines on phenylketonuria: diagnosis and treatment
Diet | Dietary advice |
---|---|
Phe-free L-amino acid supplement | Maintenance of Phe-free L-amino acid supplement intake to support protein synthesis. It is better to give smaller, frequent doses throughout the day. |
High carbohydrate intake | Encourage frequent high carbohydrate supplements, e.g. glucose polymer solution. |
Natural protein intake | In practice, a reduced appetite leads to a lower natural protein intake. |
Medications | All treatment specific medication should be continued during illness. Continue BH4 if already prescribed. Medications should be free of aspartame in PKU. |
Treat precipitating factors | e.g. anti-pyretics for pyrexia, antibiotics (aspartame-free) for bacterial infections. |