|Phe-free L-amino acid supplement||
Maintenance of Phe-free L-amino acid supplement intake to support protein synthesis.|
It is better to give smaller, frequent doses throughout the day.
|High carbohydrate intake||Encourage frequent high carbohydrate supplements, e.g. glucose polymer solution.|
|Natural protein intake||In practice, a reduced appetite leads to a lower natural protein intake.|
All treatment specific medication should be continued during illness. Continue BH4 if already prescribed.|
Medications should be free of aspartame in PKU.
|Treat precipitating factors||e.g. anti-pyretics for pyrexia, antibiotics (aspartame-free) for bacterial infections.|