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Table 1 Frequency of reported chILD diagnoses (n = 115)

From: Childhood interstitial lung diseases in immunocompetent children in Australia and New Zealand: a decade’s experience

Undefined interstitial lung disease

21

Disorders More Common in Infancy

 NEHI

15

ABCA3 deficiency

8

 Lung hypoplasia (various causes)

6

 Idiopathic bronchiolitis of infancy

4

 Surfactant protein C deficiency

4

 Nonspecific interstitial pneumonitis

4

 Acinar/Alveolar capillary dysplasia

3

 Surfactant Protein B deficiency

2

 Chronic pneumonitis of infancy

2

 Pulmonary interstitial glycogenosis

2

 Interstitial lung disease with chronic pneumonitis of infancy and possible bronchiolitis obliterans

1

 Diffuse pulmonary development disorder with patchy pulmonary interstitial glycogenosis plus bronchiolitis obliterans organizing pneumonia

1

 Cellular interstitial pneumonitis of infancy

1

Disorders of Normal Host

 Pulmonary hemosiderosis

5

 Obliterative bronchiolitis (various causes)

3

 Follicular bronchiolitis

3

 Pulmonary vasculitis/capillaritis

2

 Eosinophilic pneumonia

1

 ILD secondary to pertussis pneumonia

1

 Interstitial pneumonitis post adenovirus bronchiolitis

1

 Probable aspiration with respiratory syncytial virus infection

1

 Post infectious interstitial lung disease

1

 Idiopathic pulmonary fibrosis

1

 Pulmonary fibrosis, giant cell pneumonitis on biopsy

1

1

 Usual interstitial pneumonitis

 Desquamative interstitial pneumonitis

1

 Lymphoid interstitial pneumonia

1

 Nodular lymphoid hyperplasia

1

Disorders Related to Systemic Diseases

 ILD associated with juvenile dermatomyositis/scleroderma

4

 ILD associated with Busulphan/Melphalan/Radiation toxicity

4

 ILD with lymphangio-leiomyomatosis/Tuberous sclerosis

2

 Anti-synthetase syndrome associated with non-specific interstitial pneumonia

1

 ILD associated with mixed connective tissue disease

1

 ILD associated with Erdheim Chester disease

1

 ILD associated with Niemann Pick type B disease

1

 ILD associated with systemic sclerosis

1

 Pulmonary sarcoidosis

1

 ILD associated with Langerhans cell histiocytosis

1

  1. NEHI, Neuroendocrine hyperplasia of infancy; ABCA3, ATP-binding cassette sub-family A member 3 protein