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Table 1 Frequency of reported chILD diagnoses (n = 115)

From: Childhood interstitial lung diseases in immunocompetent children in Australia and New Zealand: a decade’s experience

Undefined interstitial lung disease 21
Disorders More Common in Infancy
 NEHI 15
ABCA3 deficiency 8
 Lung hypoplasia (various causes) 6
 Idiopathic bronchiolitis of infancy 4
 Surfactant protein C deficiency 4
 Nonspecific interstitial pneumonitis 4
 Acinar/Alveolar capillary dysplasia 3
 Surfactant Protein B deficiency 2
 Chronic pneumonitis of infancy 2
 Pulmonary interstitial glycogenosis 2
 Interstitial lung disease with chronic pneumonitis of infancy and possible bronchiolitis obliterans 1
 Diffuse pulmonary development disorder with patchy pulmonary interstitial glycogenosis plus bronchiolitis obliterans organizing pneumonia 1
 Cellular interstitial pneumonitis of infancy 1
Disorders of Normal Host
 Pulmonary hemosiderosis 5
 Obliterative bronchiolitis (various causes) 3
 Follicular bronchiolitis 3
 Pulmonary vasculitis/capillaritis 2
 Eosinophilic pneumonia 1
 ILD secondary to pertussis pneumonia 1
 Interstitial pneumonitis post adenovirus bronchiolitis 1
 Probable aspiration with respiratory syncytial virus infection 1
 Post infectious interstitial lung disease 1
 Idiopathic pulmonary fibrosis 1
 Pulmonary fibrosis, giant cell pneumonitis on biopsy 1
1
 Usual interstitial pneumonitis
 Desquamative interstitial pneumonitis 1
 Lymphoid interstitial pneumonia 1
 Nodular lymphoid hyperplasia 1
Disorders Related to Systemic Diseases
 ILD associated with juvenile dermatomyositis/scleroderma 4
 ILD associated with Busulphan/Melphalan/Radiation toxicity 4
 ILD with lymphangio-leiomyomatosis/Tuberous sclerosis 2
 Anti-synthetase syndrome associated with non-specific interstitial pneumonia 1
 ILD associated with mixed connective tissue disease 1
 ILD associated with Erdheim Chester disease 1
 ILD associated with Niemann Pick type B disease 1
 ILD associated with systemic sclerosis 1
 Pulmonary sarcoidosis 1
 ILD associated with Langerhans cell histiocytosis 1
  1. NEHI, Neuroendocrine hyperplasia of infancy; ABCA3, ATP-binding cassette sub-family A member 3 protein