Ataxia, dystonia and myoclonus in adult patients with Niemann-Pick type C

Table 4 Results of neuropsychological assessment per domain

Domain		% Patients in 1st–5th percentile	% Patients in 6th percentile or above	Number of patients
Emotion recognition^a	Total score	100	0	3
	% Patients in 1st–9th percentile	% Patients in 10th–49th percentile	% Patients in 50th percentile or above
Intelligence^b	29	43	28	7
Working memory^c	57	43	0	7
Verbal learning^d	86	14	0	7
Retention^d	29	29	42	7
Attention^e	80	20	0	5
Verbal fluency^f	100	0	0	5

^aTest used: FEEST, ^bTests used: WAIS-III, WAIS-IV, GIT-2, PPVT-III-NL, NART ^cTests used: WAIS-III digit span, WAIS-IV digit span, ^dTest used: RAVLT, ^eTest used: Trailmaking Test, ^fTests used: Fluency GIT-2, verbal fluency

ISSN: 1750-1172