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Table 3 Electrophysiological characteristics

From: Ataxia, dystonia and myoclonus in adult patients with Niemann-Pick type C

Patient Duration Frequency Location Type Back-averaging Coherence Reflex myoclonus
2 40–60 ms 0.1-10Hz Distal Positive and negative Positive Positive No
3 50–100 ms 0.1-10Hz Distal Positive and negative Positive Positive No
4 40–70 ms 0.1-10Hz Distal Positive and negative NAa Positive No
7 <70 ms 0.1-10Hz Proximal and distal Positive and negative NAa Positive No
  1. a NA not applicable