Table 3 Electrophysiological characteristics
From: Ataxia, dystonia and myoclonus in adult patients with Niemann-Pick type C
Patient | Duration | Frequency | Location | Type | Back-averaging | Coherence | Reflex myoclonus |
|---|---|---|---|---|---|---|---|
2 | 40–60 ms | 0.1-10Hz | Distal | Positive and negative | Positive | Positive | No |
3 | 50–100 ms | 0.1-10Hz | Distal | Positive and negative | Positive | Positive | No |
4 | 40–70 ms | 0.1-10Hz | Distal | Positive and negative | NAa | Positive | No |
7 | <70 ms | 0.1-10Hz | Proximal and distal | Positive and negative | NAa | Positive | No |