From: Ataxia, dystonia and myoclonus in adult patients with Niemann-Pick type C
Patient | Presenting movement disorder | Severity of current movement disorder (GCI) a | ||||
---|---|---|---|---|---|---|
Ataxia | Myoclonus | Dystonia | Tic | Overall severity | ||
1 | Ataxia | 5 | 1 | 3 | 1 | 5 |
2 | Myoclonus | 3 | 4 | 1 | 1 | 4 |
3 | Myoclonus | 2 | 3 | 1 | 1 | 3 |
4 | Myoclonus | 4 | 5 | 3 | 1 | 5 |
5 | Dystonia | 1 | 1 | 2 | 1 | 2 |
6 | Ataxia | 4 | 1 | 4 | 1 | 4 |
7 | Ataxia | 5 | 4 | 3 | 1 | 5 |
8 | Ataxia | 4 | 2 | 1 | 2 | 4 |