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Table 11 PBZ areas mean scores and clinical forms

From: Rett syndrome: a wide clinical and autonomic picture

PBZ score

Classical

Z-RTT

Hanefeld

Congenital

ARTT-NOS

Motor area

Mean (SD)

13.3 (4.6)

6.4 (3.8)

16.3 (4.5)

0 (−)

11.8 (2.3)

Range

5–24

0–15

12–22

8–14

S-C

Mean (SD)

12.2 (4.6)

8 (4.1)

21.5 (5.7)

14.2 (5.9)

Range

3–23

1–15

16–32

8–25

Daily living

Mean (SD)

10.2 8 (3.4)

5.4 (3.4)

11.8 (2.7)

7.7 (2.8)

Range

1–17

0–11

7–15

4–13

Total

Mean (SD)

35.7 (9.8)

19.8 (10.3)

49.7 (11.2)

33.7 (6)

Range

13–62

2–41

40–69

27–44