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Table 2 Repartition of reported cases among different types and subtypes of EB

From: Inherited epidermolysis bullosa and squamous cell carcinoma: a systematic review of 117 cases

Number of cases Per type EBS
3
JEB
19
DEB
88
KS
7
  Per subtype EBS-DM EBS-AR NS H-JEB nH-JEB NS DDEB RDEB 7
1 1 1 0 18 1 7 81
RDEB- HS
20
RDEB- nHS
6
RDEB-I
2
NS
53
  1. AR autosomal recessive, DDEB dominant dystrophic epidermolysis bullosa, DEB dystrophic epidermolysis bullosa, DM Dowling-Meara, EBS EB simplex, JEB junctional epidermolysis bullosa, KS Kindler syndrome, H Herlitz, HS Hallopeau-Siemens, nH non-Herlitz, nHS non Hallopeau-Siemens, RDEB recessive dystrophic epidermolysis bullosa, RDEB-I recessive dystrophic epidermolysis bullosa-Inversa, NS not specified