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Table 3 Measurements of kyphosis and scoliosis

From: Musculoskeletal manifestations in mucopolysaccharidosis type I (Hurler syndrome) following hematopoietic stem cell transplantation

No.

Age at evaluation (y)

Follow-up after HSCT (y)

Kyphotic angle (°)

Scoliotic angle (°)

Therapy

1

1.7

0

0

23

none

2

1.1

0

0

0

none

 

3.4

1.9

n.d.

0

 

3

1.2

0

30

n.d.

Brace

 

2.2

0.9

38

n.d.

 

4

2.1

0

12

35

none

5

1.5

0

14

0

none

 

3.8

2.0

33

0

 

6

0.8

8

37

n.d.

Brace

7

2.0

0

0

0

none

8

1.4

0

0

0

 
 

2.5

1.0

45

n.d.

Brace

 

3.6

2.1

52

0

 
 

5.9

4.5

57

7

 

9

4.3

2.0

10

28

Brace

 

5.1

2.9

14

24

 
 

5.7

3.5

20

19

 

10

2.2

1.0

n.d.

0

none

 

3.3

2.1

n.d.

0

 
 

4.4

3.2

n.d.

0

 

11

1.3

0

30

0

none

 

3.7

2.1

n.d.

0

 

12

1.4

0

28

8

none

 

4.6

2.7

62

16

 

13a

1.5

0

45

9

none

 

2.5

1.0

45

9

 
 

8.1

6.6

73

10

 

14

0.9

2.4

30

n.d.

Brace

 

9.6

8.6

32

40

 

15

7.8

6.8

90

n.d.

Dorsal spondylodesis at 7.8 y

16

4.2

2.4

17

9

 
 

5.2

3.4

27

n.d.

 
 

6.4

4.5

32

15

 
 

6.9

5.1

40

n.d.

Brace

 

10.8

8.9

n.d.

22

 

17

1.0

0

30

n.d.

 
 

4.5

2.7

40

n.d.

 
 

6.5

4.7

58

n.d.

Brace

 

12.5

10.7

56

19

 
 

13.8

12.0

55

15

 

18

6.2

4.1

60

n.d.

 
 

8.8

6.7

80

16

 
 

10.0

7.9

72

n.d.

Brace

19b

13.5

12.3

n.a.b

7

Dorsal spondylodesis at 14.3 y

  1. y year, n.d.not done, n.a not available
  2. aNo continuous follow-up was performed as patient lived abroad. Bracing treatment planned
  3. bPre-operative x-rays not available for review