|
UPN
|
Age (years)
|
Gender
|
Ethnicitya
|
Treatmentb
|
CT
|
Spirometry
|
IOS
|
|---|
|
1-ADA26
|
3
|
F
|
C
|
1
|
ND
|
-
|
+
|
|
2-ADA41
|
5
|
F
|
C
|
2
|
ND
|
-
|
+
|
|
3-ADA14
|
8
|
F
|
C
|
2
|
Normal
|
+
|
+
|
|
4-ADA16
|
9
|
M
|
H
|
1
|
dGGO, MA, B
|
-
|
+
|
|
5-ADA18
|
10
|
F
|
A
|
2
|
ND
|
+
|
+
|
|
6-ADA5
|
12
|
M
|
AA
|
1
|
MA
|
+
|
+
|
|
7-ADA46
|
14
|
F
|
C
|
2
|
dGGO, PC, MA, N
|
-
|
+
|
|
8-ADA17
|
16
|
F
|
AA
|
2
|
MA
|
-
|
+
|
|
9-ADA3
|
17
|
M
|
C
|
2
|
dGGO, PC
|
+
|
+
|
|
10-ADA47
|
18
|
M
|
AA
|
2
|
ND
|
+
|
+
|
-
aC = Caucasian, H = Hispanic, A = Asian, AA = African American
-
b1 = Gene Therapy; 2 = ADA conjugated with polyethylene glycol (PEG-ADA)
- CT findings: ND CT not performed, dGGO diffuse ground glass opacities, PC parenchymal Cysts, MA Mosaic attenuation, B Bronchiectasis, N Nodules
- + Indicates successful completion of Spirometry and/or IOS
