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Table 1 Patient characteristics and pulmonary imaging and function testing

From: Impulse oscillometry identifies peripheral airway dysfunction in children with adenosine deaminase deficiency

UPN Age (years) Gender Ethnicitya Treatmentb CT Spirometry IOS
1-ADA26 3 F C 1 ND - +
2-ADA41 5 F C 2 ND - +
3-ADA14 8 F C 2 Normal + +
4-ADA16 9 M H 1 dGGO, MA, B - +
5-ADA18 10 F A 2 ND + +
6-ADA5 12 M AA 1 MA + +
7-ADA46 14 F C 2 dGGO, PC, MA, N - +
8-ADA17 16 F AA 2 MA - +
9-ADA3 17 M C 2 dGGO, PC + +
10-ADA47 18 M AA 2 ND + +
  1. aC = Caucasian, H = Hispanic, A = Asian, AA = African American
  2. b1 = Gene Therapy; 2 = ADA conjugated with polyethylene glycol (PEG-ADA)
  3. CT findings: ND CT not performed, dGGO diffuse ground glass opacities, PC parenchymal Cysts, MA Mosaic attenuation, B Bronchiectasis, N Nodules
  4. + Indicates successful completion of Spirometry and/or IOS