Table 7 Dietary treatment in the 14 Austrian patients with LCHADD, calculated from a dietary protocol
Patient | Age at evaluation | Body weight (kg) | Total fat intake | % MCT of fat in diet | Walnut oil (in ml and g/kg/d) | Heptanoate (C7) (in ml and g/kg/d) | C7 since | DHA suppl. | kcal/d |
|---|---|---|---|---|---|---|---|---|---|
1 | 15.0 y | 72,6 | 30% | 20% | 0 ml | - | +267 mg | 3000 | |
2 | 13.5 y | 55.5 | 40% | 50% | 5 ml = 0.10 | 30 ml = 0.60 | 9.4 y | - | 1800 |
3 | 10.0 y | 29.7 | 33.5% | 72% | 10 ml = 0.34 | - | +89 mg | 1700 | |
4 | 7.2 y | 24.9 | 25% | 52% | 10 ml = 0.40 | 20 ml = 0.80 | 7 y | - | 1738 |
5 | 7.3 y | 29.0 | 27% | 56% | 3 ml = 0.10 | - | *200 mg | 1653 | |
6 | 2.7 y | 13.3 | 36% | 47% | 6 ml = 0.45 | 10 ml = 0.75 | 13 m | - | 953 |
7 | 10.6 y | 36.9 | 29% | 69% | 10 ml = 0.27 | - | +89 mg | 1900 | |
8 # | 4.0 y | 17.4 | 15% | 80% | 10 ml = 0.57 | 10 ml = 0.60 | 13 m | - | 1452 |
9 | 10.7 y | 25.0 | 21% | 68% | 2 ml = 0.08 | - | *200 mg | 1850 | |
10 | 9.3 y | 25.1 | 28% | 70% | 13 ml = 0.52 | - | *100 mg | 1782 | |
11 | 3.7 y | 15.4 | 25% | 64% | 13 ml = 0.84 | - | +89 mg | 1300 | |
12 | 2.8 y | 15.3 | 30% | 63% | 4 ml = 0.26 | - | *100 mg | 1377 | |
13 | 2.7 y | 11.1 | 30% | 61% | 3 ml = 0.27 | - | *150 mg | 1166 | |
14 | 0.9 y | 8.62 | 33% | 65% | 3 ml = 0.35 | - | *150 mg | 862 | |
Median | 5.6 y | 28.5% | 62% | 0.34 | |||||
Range | 0.9 – 15.0 | 15 – 40 | 20 – 80 | 0.08 – 0.84 |