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Table 1 Prevalence of sporadic IBM in different populations

From: Sporadic inclusion body myositis: the genetic contributions to the pathogenesis

Study

Region

Diagnostic criteria

Prevalence (per million population)

Prevalence > 50 yrs (per million population)

Lingberg et al.[2]

Sweden

Biopsy and clinical data

2.2

n/a

Kaipiainen-Seppanen and Aho[4]

Finland

Not mentioned

0.9

n/a

Philips et al.[5]

Australia

Griggs et al. criteria

9.3

35.3

Badrising et al.[3]

Netherlands

ENMC criteria

4.9

16

Felice and North (Connecticut, USA)[6]

Connecticut, USA

Griggs et al. criteria

10.7

28.9 (>45 yrs)

Needham et al.[1]

Western Australia

Clinical and biopsy criteria

14.9

51.2

Wilson et al.[7]

Olmsted County, USA

Griggs et al. criteria

71

n/a

Oflazer et al.[8]

Istanbul, Turkey

Own criteria from the study (biopsy and clinical data)

1.0

6.0

Suzuki et al.[9]

Japan

Clinical and biopsy criteria

1.3 (in 1991)

n/a

9.8 (in 2003)

n/a

Tan et al.[10]

South Australia

Biopsy and clinical data

50.5

139.3