Pulmonary alveolar proteinosis in children on La Réunion Island: a new inherited disorder?

Table 4 Radiological features

	Diagnosis CT	Last available CT
	*n =* 17	*n =* 13
Age (median (IQR))	10 m (4.5 m – 22 y)	10 y (4.1 y – 14.1 y)
Elementary lesions n (%)
Ground glass opacity	16 (94)	13 (100)
Consolidation	13 (76)	1 (8)
Interlobular septal thickening	17 (100)	13 (100)
Intralobular lines	17 (100)	13 (100)
Distension	13 (76)	1 (8)
Fissures thickening	16 (94)	13 (100)
Micronodules	1 (6)	0 (0)
Cystic lesions	1 (6)	12 (92)
Traction bronchiectasis	1 (6)	11 (85)
Honeycombing	1 (6)	5 (40)

Data are presented at diagnosis and for the last available CT scan. Observed lesions are reported according to the Fleischner Society’s Glossary of Terms for Thoracic Imaging (32). At diagnosis, ground glass opacities, interlobular thickening, intralobular lines and consolidations are the proeminent features. At last follow-up, consolidations have disappeared and fibrotic lesions are almost constant.

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