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Table 1 Prevalence, incidence, mortality and fatality rates by age group

From: A population-based registry as a source of health indicators for rare diseases: the ten-year experience of the Veneto Region’s rare diseases registry

 

Prevalence per 10,000

Crude incidence per 10,000

Mortality per 100,000

Fatality per 1,000

Age

Rate

C.I. 95%

Rate

C.I. 95%

Rate

C.I. 95%

Rate

C.I. 95%

0-17 years

44.05

42.61-45.49

3.96

3.52-4.39

10.21

8.01-12.41

3.59

1.37-5.81

0-12 months

25.73

21.23-30.24

25.73

21.23-30.24

0.56*

0.35*-0.77*

19.23

4.74-33.72

1-17 years

45.22

43.71-46.72

4.26

3.80-4.73

7.29

6.69-7.90

2.98

0.92-5.04

1-14 years

46.25

44.58-47.93

4.41

3.89-4.92

8.00

7.30-8.69

3.10

0.81-5.39

15-17 years

40.26

36.84-43.68

3.57

2.55-4.59

3.93

2.86-5.00

2.36

0.00-6.99

18-64 years

31.34

30.72-31.96

3.70

3.48-3.91

9.03

7.97-10.09

3.70

2.33-5.07

over 65 years

17.68

16.83-18.53

2.90

2.56-3.25

28.51

25.10-31.91

26.79

17.49-36.10

TOTAL

33.09

32.56-33.62

3.85

3.67-4.03

13.04

12.02-14.06

5.99

4.58-7.40

  1. Veneto Region’s rare diseases registry. * rate per 1,000 live births.