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Figure 4 | Orphanet Journal of Rare Diseases

Figure 4

From: Arginine improves peroxisome functioning in cells from patients with a mild peroxisome biogenesis disorder

Figure 4

Catalase immunofluorescence in PEX1, PEX6 and PEX12 deficient fibroblasts incubated with arginine. Shown is the effect of 21 days incubation with 20 mM arginine on the three different PEX1-G843D cell lines and a PEX6 and a PEX12 patient cell line. Two independent cover slips per condition were examined by counting the number of cells with catalase-containing peroxisomes among at least 200 cells. Control (C) showed 100% peroxisome-positive cells. PEX1-I700fsX41 (negative control = ZS) displayed no peroxisome-positive cells. The data are presented as mean±SD.

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Orphanet Journal of Rare Diseases

ISSN: 1750-1172