Table 1 Clinical and serological findings in patients with recessive dystrophic epidermolysis bullosa (RDEB) and with epidermolysis bullosa simplex (EBS)

Patients, no.

17

10

Mean Age

21

17

Range years

2-50

1-56

Males/Females

4/13

3/7

Birmingham severity score

Birmingham severity score, mean

55

5.4

Birmingham severity score, range

5-90

2-36

Autoantibodies titres, mean concentrations

P*

-Anti-type VII collagen (U/mL)

27.8

2.5

0.0014

-Anti-BP180 (U/mL)

59.4

8.3

0.0028

-Anti-BP230 (U/mL)

51.2

6.6

0.0023