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Table 1 Clinical and serological findings in patients with recessive dystrophic epidermolysis bullosa (RDEB) and with epidermolysis bullosa simplex (EBS)

From: Prevalence of specific anti-skin autoantibodies in a cohort of patients with inherited epidermolysis bullosa

  Patients with RDEB Patients with EBS  
Patients, no. 17 10  
Mean Age 21 17  
Range years 2-50 1-56  
Males/Females 4/13 3/7  
Birmingham severity score  
Birmingham severity score, mean 55 5.4  
Birmingham severity score, range 5-90 2-36  
Autoantibodies titres, mean concentrations P*
-Anti-type VII collagen (U/mL) 27.8 2.5 0.0014
-Anti-BP180 (U/mL) 59.4 8.3 0.0028
-Anti-BP230 (U/mL) 51.2 6.6 0.0023
  1. * Unpaired T Test, P-value < 0.05 was considered statistically significant.