Table 1 Patient characteristics
From: The impact of Hunter syndrome (mucopolysaccharidosis type II) on health-related quality of life
| Â | Mean | SD | Median | Min | Max | % Missing |
|---|---|---|---|---|---|---|
All patients (N = 96) | ||||||
Age (yrs) | 14.2 | 6.7 | 13.6 | 5.0 | 30.9 | 0.0 |
Age at diagnosis (yrs) | 4.3 | 3.7 | 3.0 | 0.0 | 20.0 | 2.1 |
Duration of MPS II (yrs) | 9.8 | 6.8 | 8.5 | 0.3 | 26.0 | 2.1 |
Height (cm) | 127.8 | 14.8 | 126.5 | 99.06 | 170.0 | 12.5 |
Weight (kg) | 35.9 | 13.2 | 32.7 | 19.0 | 78.0 | 7.3 |
6MWT (m) | 400.3 | 100.3 | 407.5 | 37.0 | 588.0 | 2.1 |
% predicted FVC | 56.2 | 14.9 | 54.8 | 16.0 | 90.8 | 2.1 |
Global JROM score (%) | 67.3 | 9.1 | 67.8 | 43.4 | 87.2 | 1.0 |
Patients above 12 years old who completed self-report questionnaires (N = 53) | ||||||
Age (yrs) | 19.2 | 4.8 | 18.7 | 12.1 | 30.9 | 0.0 |
Age at diagnosis (yrs) | 5.5 | 4.5 | 4.0 | 0.0 | 20.0 | 3.8 |
Duration of MPS II (yrs) | 13.6 | 6.9 | 12.6 | 0.5 | 26.0 | 3.8 |
Height (cm) | 135.1 | 13.8 | 132.5 | 109.2 | 170.0 | 11.3 |
Weight (kg) | 43.6 | 12.9 | 38.8 | 26.8 | 78.0 | 9.4 |
6MWT (m) | 377.9 | 116.5 | 395.0 | 37.0 | 588.0 | 1.9 |
% predicted FVC | 50.1 | 13.1 | 50.0 | 16.0 | 79.2 | 1.9 |
Global JROM score (%) | 62.4 | 7.4 | 62.8 | 43.4 | 82.3 | 1.9 |