Skip to main content
Figure 1 | Orphanet Journal of Rare Diseases

Figure 1

From: Copper and bezafibrate cooperate to rescue cytochrome c oxidase deficiency in cells of patients with sco2 mutations

Figure 1

A) RC enzyme activities in HeLa Cells treated with 400 μM BZF. HeLa cells were incubated for 5 days with 400 μM BZF and then assayed for RC complex activities. * = significant difference versus untreated (p<0.05). B) HEK293, primary skin fibrolasts and SEM cells (a leukaemia cell line) were treated with 400 μM BZF as in panel A and then assayed for COX activity. We did not detect significant changes in CS activity in any cell line after BZF tretment.

Back to article page

Orphanet Journal of Rare Diseases

ISSN: 1750-1172