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Table 2 A list of major IgG4-related disease in various organs.

From: Type 1 autoimmune pancreatitis

Organ

Manifestation

Pituitary gland

Hypophysitis

Meningis

Pachymeningitis

Lacrimal gland

Chronic sclerosing dacryoadenitis (Mikulicz's disease)

Salivary gland

Chronic sclerosing sialadenitis (Küttner's tumour)

Lymph node

Lymphadenopathy with 5 histological subtypes

 

   - Multicentric Castleman disease-like (type I)

 

   - Follicular hyperplasia (type II)

 

   - Interfollicular expansion (type III)

 

   - Progressive transformation of germinal centre (type IV)

 

   - Nodal inflammatory pseudotumor (type V)

Thyroid

Thyroiditis or hypothyroidism

Skin

Pseudolymphoma

Breast

Inflammatory pseudotumour or mastitis

Lung

Inflammatory pseudotumour

 

Focal or diffuse interstitial pneumonia

 

Inflammation in bronchovascular bundles.

Pleura

Nodular pleuritis

Stomach

Chronic gastritis or ulcer

Vater's ampulla

Pseudotumourous enlargement

Pancreas

Type 1 autoimmune pancreatitis

Bile duct

Sclerosing cholangitis

Gallbladder

Lymphoplasmacytic sclerosing cholecystitis

Liver

Inflammatory pseudotumour

 

Chronic active hepatitis (autoimmune hepatitis)

Retroperitoneum

Retroperitoneal fibrosis

Aorta/artery

Periaortitis/periarteritis

 

Inflammatory aneurysm

Kidney

Tubulointerstitial nephritis

Peripheral nerve

Perineural mass