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Table 2 A list of major IgG4-related disease in various organs.

From: Type 1 autoimmune pancreatitis

Organ Manifestation
Pituitary gland Hypophysitis
Meningis Pachymeningitis
Lacrimal gland Chronic sclerosing dacryoadenitis (Mikulicz's disease)
Salivary gland Chronic sclerosing sialadenitis (Küttner's tumour)
Lymph node Lymphadenopathy with 5 histological subtypes
     - Multicentric Castleman disease-like (type I)
     - Follicular hyperplasia (type II)
     - Interfollicular expansion (type III)
     - Progressive transformation of germinal centre (type IV)
     - Nodal inflammatory pseudotumor (type V)
Thyroid Thyroiditis or hypothyroidism
Skin Pseudolymphoma
Breast Inflammatory pseudotumour or mastitis
Lung Inflammatory pseudotumour
  Focal or diffuse interstitial pneumonia
  Inflammation in bronchovascular bundles.
Pleura Nodular pleuritis
Stomach Chronic gastritis or ulcer
Vater's ampulla Pseudotumourous enlargement
Pancreas Type 1 autoimmune pancreatitis
Bile duct Sclerosing cholangitis
Gallbladder Lymphoplasmacytic sclerosing cholecystitis
Liver Inflammatory pseudotumour
  Chronic active hepatitis (autoimmune hepatitis)
Retroperitoneum Retroperitoneal fibrosis
Aorta/artery Periaortitis/periarteritis
  Inflammatory aneurysm
Kidney Tubulointerstitial nephritis
Peripheral nerve Perineural mass