Table 4 Similarities in pulmonary involvement between Behcet's disease and HSS (adapted from Erkan et al [38])
From: Hughes-Stovin Syndrome
Characteristic | Details |
|---|---|
Gender | Predominantly young males |
Triad of clinical findings | Fever, arthalgias, thrombosis |
Occurrence of thrombosis with pulmonary artery aneurysms | HSS - 100%; Behcet's disease - 80% |
Overlapping histopathologic features | Destruction of arterial walls, perivascular infiltrates |
Therapy | Cytotoxic drugs and corticosteroids |
Most common cause of death | Rupture of pulmonary artery aneurysm |