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Table 4 Similarities in pulmonary involvement between Behcet's disease and HSS (adapted from Erkan et al [38])

From: Hughes-Stovin Syndrome

Characteristic Details
Gender Predominantly young males
Triad of clinical findings Fever, arthalgias, thrombosis
Occurrence of thrombosis with pulmonary artery aneurysms HSS - 100%; Behcet's disease - 80%
Overlapping histopathologic features Destruction of arterial walls, perivascular infiltrates
Therapy Cytotoxic drugs and corticosteroids
Most common cause of death Rupture of pulmonary artery aneurysm