Table 3 NF1-associated deaths by underlying cause

   Malignant neoplasms (ICD-9:140-208; ICD10: C00-C97)

Lip, oral cavity and pharynx (ICD-9:140-149; ICD10: C00-C14)

Colorectal (ICD-9:153-154; ICD-10: C18-C21)

Stomach (ICD-9:151; ICD10: C16)

Liver and intrahepatic bile ducts (ICD-9:155; ICD10: C22)

Pancreas (ICD-9:157; ICD10: C25)

Trachea/bronchus/lung (ICD-9:162; ICD-10: C33-C34)

Bone and articular cartilage (ICD-9:170; ICD-10: C40-C41)

Connective and other soft tissue (ICD-9:171; ICD-10: C49)

Skin (malignant melanoma) (ICD-9:172: ICD-10: C43)

Breast (ICD-9:174-175; ICD-10: C50)

Body (or unspecified part) of uterus (ICD-9:179; 182; ICD-10: C54-C55)

Cervix uteri (ICD-9:180; ICD-10: C53)

Ovary (ICD-9:183.0; ICD-10: C56)

Prostate (ICD-9:185; ICD-10: C61)

Kidney, except pelvis (ICD-9:189.0; ICD-10: C64)

Bladder (ICD-9:188; ICD-10: C67)

Brain (ICD-9:191; ICD-10: C71)

Other and unspecified parts of nervous system (ICD-9:192; ICD-10: C70; C72)

Other and ill-defined sites (ICD-9:195; ICD-10: C76)

Neoplasm without specification of site (ICD-9:199; ICD-10: C80)

Lymphatic and hematopoietic tissue (ICD-9: 200-208; ICD-10: C81-C96)

Malignant neoplasms (excluding those of connective and soft tissue, brain, other and unspecified parts of nervous system, or other and ill-defined sites)

   Benign Neoplasms (ICD-9:210-229; ICD-10: D10-D36)

   Neoplasms of uncertain behavior and unspecified nature, excluding neurofibromatosis (ICD-9: 235-239, excluding 237.7; ICD-10: D37-D48)

Infectious and parasitic diseases, including AIDS (ICD-9: 1-139, 279.1; ICD-10: A00-B99)

Endocrine, nutritional and metabolic diseases (ICD-9: 240-278 ICD-10: E00-E90)

Diabetes mellitus (ICD-9: 250; ICD-10: E10-E14)

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism, excluding AIDS (ICD-9: 279-289; excluding 279.1; ICD-10: D50-D89)

Mental disorders (ICD-9: 290-319; ICD-10: F00-F99)

Diseases of the nervous system and sense organs (ICD-9: 320-389; ICD-10: G00-H95)

Diseases of the circulatory system (ICD-9: 390-459; ICD-10: I00-I99 )

Hypertensive disease (ICD-9: 401-405; ICD-10: I10-I15)

Ischemic heart disease (ICD-9: 410-414; ICD-10: I20-I25)

Cerebrovascular disease (ICD-9: 430-438; ICD-10: I60-I69)

Diseases of the respiratory system (ICD-9: 460-519; ICD-10: J00-J99)

Obstructive chronic bronchitis (ICD-9: 491.2; ICD-10: J448)

Diseases of the digestive system (ICD-9: 520-579; ICD-10: K00-K93 )

Diseases of the genitourinary system (ICD-9: 580-629; ICD-10: N00-N99)

Diseases of the skin and subcutaneous tissue (ICD-9: 680-709; ICD-10: L00-L99)

Diseases of the musculoskeletal system and connective tissue (ICD-9:710-739; ICD-10: M00-M99)

Congenital anomalies, excluding neurofibromatosis (ICD-9:740-759; ICD-10: Q00-Q99, excluding Q85.0)

Injury and poisoning (ICD-9: 800-999; ICD-10: S00-T98)

TOTAL