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Table 6 Differential diagnosis of inherited EB (in neonates and small children) *

From: Inherited epidermolysis bullosa

Inherited or congenital disorders

 
 

Epidermolytic hyperkeratosis (bullous congenital ichthyosiform erythroderma)

 

Ichthyosis bullosa of Siemens

 

Peeling skin syndrome

 

Pachyonychia congenita

 

Congenital porphyrias

 

Acrodermatitis enteropathica

 

Incontinentia pigmentii

 

Ectodermal dysplasia (ED)

 

   AEC syndrome (Hay-Wells syndrome)

 

Congenital absence of skin (cutis aplasia)

 

Congenital erosive dermatosis with reticulate supple scarring

Acquired disorders

 
 

Immunobullous disorders

 

   EB acquisita

 

   Linear IgA dermatosis

 

   Bullous pemphigoid

 

   Cicatricial pemphigoid

 

   Neonatal herpes gestationis

 

   Pemphigus

 

Infectious diseases

 

   Herpes simplex

 

   Staphylococcal scalded skin syndrome

 

   Bullous impetigo

 

Other diseases or conditions

 

   Bullous mastocytosis

 

   Traumatic blisters (sucking; other)

  1. * modified from Fine JD et al, 2000 [5]