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Table 2 Clinical and radiographic features of dentinogenesis imperfecta and dentine dysplasia [4, 9, 50–53].

From: Hereditary dentine disorders: dentinogenesis imperfecta and dentine dysplasia

Dental features DGI I DGI II DGI III DD I DD II
Osteogenesis
Imperfecta 		+     
Amber translucent (opalescent) + + +/-   +1
Attrition + + +/-   +1
Bulbous crowns   + +/-   +1
Cervical constriction   + +/-   +1
Pulp exposures    +   
Periapical radiolucencies    + +  
Shell teeth    +   
Normal roots      +
Short constricted roots + + +/-   +1
Sharp conical short roots     +  
Rootless teeth     +  
Pulp obliteration primary +/- +   + +
Pulp obliteration permanent +/- +    
Partially obliterated crescent shaped pulp chamber
Permanent 		    +  
Thistle tubed pulp chamber      +/-2
Pulp stones     +/- +/-2
Primary Dentition affected + + + + +
Permanent dentition affected + + + + +/-
No clinical features     + +2
Variable expression +   +   +
  1. 1 Primary Dentition.2 Permanent dentition.
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Orphanet Journal of Rare Diseases

ISSN: 1750-1172