Skip to main content

Table 1 Baseline characteristics

From: Lung function decline preceding chronic respiratory failure in spinal muscular atrophy: a national prospective cohort study

SMA type

1c

2a

2b

3a

Number of patients

8

20

7

3

Age (years) at start ventilation

20.45

15.98

24.80

47.75

Median (IQR)

(14.25; 23.60)

(12.86; 27.61)

(16.16; 28.08)

(41.80; 55.20)

Ventilatory support started electively, n (%)

6 (75)

16 (80)

4 (57)

3 (100)

Symptoms nocturnal hypoventilation, n (%)

2 (25)

5 (25)

1 (14)

0 (0)

Years between test and start ventilation

0.4

0.2

4.5

0.6

median (IQR)

(0.1; 1.0)

(0.1; 0.7)

(0.1; 5.8)

(0.2; 0.7)

  1. IQR = Interquartile range; n = number