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Table 4 Median energy, total protein, natural protein, and protein equivalent intake from phenylalanine-free infant amino acid formula

From: Phenylalanine free infant formula in the dietary management of phenylketonuria

 

Energy intake

Protein intake

EAR %

kcal/kg/d

kcal/d

% kcal from the study formula

Total (g/d)

Total (g/kg/d)

PE (g/d) from Phe-free infant formula b

PE (g/kg/d) from Phe-free infant formulab

% From Phe-free infant formula

Natural (g/d)

Natural (g/kg/d)

Baseline (n = 9)a

110 (91–115)

104 (92–111)

618 (547–746)

50 (45–57)

18 (14–31)

3.1 (2.7–3.5)

11 (8–13)

1.3 (1.2–1.9)

55 (34–62)

5.9 (5.9–6.0)

0.8 (0.6–1.0)

Short-term (28-day)

Evaluation (n = 8)a

103 (85–110)

91 (81–101)

662 (632–803)

54 (51–65)

18 (16–24)

2.5 (2.3–2.7)

12 (9–15)

1.5 (1.3–1.7)

62 (58–74)

5.3 (4.4–5.9)

0.6 (0.5–0.8)

Extension study (12-month) follow-up (n = 7)

90 (79–101)

84 (68–96)

662 (620- 797)

59 (51–62)

21 (17–31)

2.5 (2.0–3.2)

11 (8–12)

1.0 (0.6–1.4)

49 (31–65)

4.8 (4.5–5.5)

0.5 (0.4–0.6)

Mean (n = 9)

94 (81–109)

90 (74–101)

662 (605–792)

57 (50–62)

19 (17–31)

2.6 (2.1–3.2)

11 (8–13)

1.2 (0.8–1.6)

53 (33–66)

5.1 (4.5–5.9)

0.6 (0.4–0.7)

  1. EAR, estimated average requirements; Phe, phenylalanine; PE, protein equivalent
  2. aOne breastfed infant was not included
  3. bProtein equivalent intake from phenylalanine-free infant amino acid formula only (excluding weaning protein substitute)