From: Phenylalanine free infant formula in the dietary management of phenylketonuria
 | Energy intake | Protein intake | |||||||||
---|---|---|---|---|---|---|---|---|---|---|---|
EAR % | kcal/kg/d | kcal/d | % kcal from the study formula | Total (g/d) | Total (g/kg/d) | PE (g/d) from Phe-free infant formula b | PE (g/kg/d) from Phe-free infant formulab | % From Phe-free infant formula | Natural (g/d) | Natural (g/kg/d) | |
Baseline (n = 9)a | 110 (91–115) | 104 (92–111) | 618 (547–746) | 50 (45–57) | 18 (14–31) | 3.1 (2.7–3.5) | 11 (8–13) | 1.3 (1.2–1.9) | 55 (34–62) | 5.9 (5.9–6.0) | 0.8 (0.6–1.0) |
Short-term (28-day) Evaluation (n = 8)a | 103 (85–110) | 91 (81–101) | 662 (632–803) | 54 (51–65) | 18 (16–24) | 2.5 (2.3–2.7) | 12 (9–15) | 1.5 (1.3–1.7) | 62 (58–74) | 5.3 (4.4–5.9) | 0.6 (0.5–0.8) |
Extension study (12-month) follow-up (n = 7) | 90 (79–101) | 84 (68–96) | 662 (620- 797) | 59 (51–62) | 21 (17–31) | 2.5 (2.0–3.2) | 11 (8–12) | 1.0 (0.6–1.4) | 49 (31–65) | 4.8 (4.5–5.5) | 0.5 (0.4–0.6) |
Mean (n = 9) | 94 (81–109) | 90 (74–101) | 662 (605–792) | 57 (50–62) | 19 (17–31) | 2.6 (2.1–3.2) | 11 (8–13) | 1.2 (0.8–1.6) | 53 (33–66) | 5.1 (4.5–5.9) | 0.6 (0.4–0.7) |