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Table 1 Nutritional composition of the phenylalanine-free infant amino acid formula used in the study: comparison with pre-baseline phenylalanine-free infant amino acid formula, and breast milk

From: Phenylalanine free infant formula in the dietary management of phenylketonuria

Nutritional Information (per 100 ml)

Units

PKU Starta (Vitaflo)

PKU Anamix infantb (Nutricia)

Mature breast milkc

Energy

kcal

68

70

70

 

kj

287

293

291

Protein equivalent

g

2.0

2.0

1.07

Carbohydrate

g

7.1

7.5

7.4

 Of which sugars

g

0.7

1.1

 

Fat

G

3.5

3.5

4.2

 Of which DHA

mg

14

17.8

13.6

 Of which AA

mg

28

17.8

17.6

Vitamins

    

 Vitamin A

µg RE

64

61.2

60

 Vitamin D

µg

1.6

1.7

0.01

 Vitamin E

mg αTE

0.84

1.38

0.35

 Vitamin C

mg

8.6

7.34

3.8

 Vitamin K

µg

5.6

5.59

N/A

 Thiamin

mg

0.06

0.08

0.01

 Riboflavin

mg

0.07

0.08

0.03

 Niacin

mg

0.46

0.35

0.23

 Niacin equivalents

mg NE

1.1

0.57

0.62

 Vitamin B6

mg

0.06

0.08

0.06

 Folic acid

µg

10.8

8.25

5.2

 Vitamin B12

µg

0.17

0.18

0.01

 Biotin

µg

2.7

2.7

0.8

 Pantothenic acid

mg

0.35

0.42

0.26

 Choline

mg

21.3

21.9

N/A

Minerals

    

 Sodium

mg

27

28.7

15

 Potassium

mg

71

75.8

60

 Chloride

mg

51

53.3

43

 Calcium

mg

56

61.5

35

 Phosphorus

mg

42

45

15

 Magnesium

mg

6.3

8.8

2.8

Trace elements

    

 Iron

mg

0.81

1.19

0.07

 Copper

µg

56

63

39

 Zinc

mg

0.49

0.84

0.3

 Manganese

mg

0.04

0.004

N/A

 Iodine

µg

14.8

14.7

7

 Molybdenum

µg

2.2

1.82

N/A

 Selenium

µg

3.0

2.7

1.4

 Chromium

µg

1.8

2.1

N/A

Amino acids

    

 Alanine

g

0.08

0.09

0.05

 Arginine

g

0.14

0.16

0.05

 Aspartic acid

g

0.22

0.15

N/A

 Cystine

g

0.05

0.06

0.03

 Glutamine

g

0.16

0.21

0.23

 Glycine

g

0.21

0.14

0.03

 Histidine

g

0.08

0.09

0.03

 Isoleucine

g

0.15

0.14

0.07

 Leucine

g

0.23

0.24

0.12

 Lysine

g

0.15

0.17

0.09

 Methionine

g

0.04

0.04

0.02

 Phenylalanine

g

0.00

0.00

0.05

 Proline

g

0.15

0.17

0.12

 Serine

g

0.10

0.11

0.05

 Threonine

g

0.15

0.12

0.05

 Tryptophan

g

0.05

0.05

0.03

 Tyrosine

g

0.22

0.22

0.04

 Valine

g

0.17

0.16

0.09

  1. PKU, phenylketonuria; DHA, docosahexaenoic acid; AA, arachidonic acid; N/A, not applicable
  2. aAt standard dilution of 14.1%
  3. bAt standard dilution of 15.0%
  4. cValues are from Oppe, 1977. DHA and AA contents were calculated from Giuffrida et al. (2022)