Variable | Proband | The proband’s brother | Normal range |
---|---|---|---|
WBC (× 109/L) | 22.82 | 16.1 | 3.5–9.5 |
Hb (g/L) | 113 | 73 | 120–160 |
PLT (× 109/L) | 22 | 44 | 125–350 |
IgG (g/L) | 6.3 | 18.10 | 7.5–15 |
IgA (g/L) | 0.02 | 0.76 | 1.0–5 |
IgM (g/L) | 0.12 | 1.6 | 0.46–3 |
IgE (mg/L) | 2.9 | 4.93 | 0.1–0.9 |
EBV-DNA (× 103 IU) | 2 | Negative | < 1 |
HCMV-DNA (× 103 IU) | Negative | 8.027 | < 0.5 |
total T cell (%) | 52.1 | 85.8 | 20–50 |
CD3 + (%) | 48.8 | – | 56–86 |
CD3 + CD4 + (%) | 34.4 | 12.4 | 33–58 |
CD3 + CD8 + (%) | 13.5 | 36.8 | 20–39 |
CD3 + CD4 + /CD3 + CD8 + (%) | 2.55 | 0.3 | 0.7–2.5 |
CD19 + /20 + (%) | 7.7 | – | 5–18 |
CD3-CD56 + (%) | 34.3 | 7.8 | 10–20 |