Table 3 The glycine index in nonketotic hyperglycinemia during ketogenic diet
Treatment | Weight (Kg) | Benzoate (mg/kg/day) | Glycine intake (mg/day) | Glycine index (mmol/kg/day) |
|---|---|---|---|---|
Patient 1 | ||||
Benzoate | 3.42 | 450 | 128 | − 2.62 |
Benzoate | 7.738 | 434 | 302 | − 2.49 |
KD | 8.705 | 230 | 210 | − 1.27 |
Patient 2 | ||||
Benzoate | 3.415 | 609 | 163 | − 3.59 |
KD | 4.17 | 264 | 273 | − 0.96 |
Benzoate | 4.25 | 602 | 178 | − 3.62 |
Patient 4 | ||||
Benzoate | 13.6 | 600 | 380 | − 3.79 |
KD | 17.8 | 300 | 35 | − 2.06 |