From: Lung and chest wall volume during vital capacity manoeuvre in Osteogenesis Imperfecta
 |  | Healthy | OI Type III | OI Type I-IV | Healthy vs. OI Type III | Healthy vs. OI Type I-IV | OI Type III vs. OI Type I-IV |
---|---|---|---|---|---|---|---|
volume | pulmonary rib cage [L] | 10.23 (3.29) | 4.41 (4.71) | 9.2 (2.28) | 0.001 | 0.227 | 0.005 |
pulmonary rib cage [% chest wall] | 51.5 (8.4) | 48.8 (9.1) | 55.1 (20.4) | 0.198 | 1.000 | 0.382 | |
abdominal rib cage [L] | 3.24 (2.1) | 2 (1.25) | 2.85 (2.33) | 0.006 | 0.307 | 0.123 | |
abdominal rib cage [% chest wall] | 18.8 (6.2) | 15.7 (5.9) | 15.4 (10) | 0.561 | 0.378 | 0.328 | |
abdomen [L] | 5.42 (3.06) | 3.35 (3.62) | 5.34 (5.16) | 0.046 | 0.853 | 0.181 | |
abdomen [% chest wall] | 29.1 (6.5) | 34.1 (7.5) | 28.3 (13) | 0.051 | 0.853 | 0.572 | |
chest wall [L] | 20.07 (7.24) | 9.89 (9.92) | 18.1 (11.66) | 0.005 | 0.642 | 0.018 | |
 | trunk height [cm] | 39.4 (4.3) | 23.1 (4) | 30.8 (5.3) | 0.000 | 0.000 | 0.000 |
diameters | AP at angle of Louis level [cm] | 18.5 (2.6) | 18.2 (5.1) | 19.2 (3.3) | 0.868 | 0.246 | 0.304 |
AP at xiphoid level [cm] | 22.9 (3.2) | 23.7 (6.9) | 26 (4.8) | 0.318 | 0.041 | 0.504 | |
AP at umbilical level [cm] | 22 (4.5) | 27.2 (8.3) | 26.2 (13.1) | 0.067 | 0.023 | 0.837 | |
ML at angle of Louis level [cm] | 26.8 (3.4) | 22.7 (8.3) | 27.5 (4) | 0.212 | 0.265 | 0.111 | |
ML at xiphoid level [cm] | 27.2 (2.9) | 25.5 (6.7) | 29.5 (5.1) | 0.868 | 0.137 | 0.217 | |
ML at umbilical level [cm] | 26.7 (4.1) | 26.4 (6.4) | 29 (8.5) | 0.835 | 0.246 | 0.355 | |
AP/ML at angle of Louis level | 0.7 (0.11) | 0.75 (0.19) | 0.71 (0.05) | 0.124 | 0.676 | 0.136 | |
AP/ML at xiphoid level | 0.86 (0.1) | 0.9 (0.1) | 0.89 (0.05) | 0.280 | 0.150 | 0.959 | |
AP/ML at umbilical level | 0.83 (0.05) | 0.99 (0.17) | 0.9 (0.14) | 0.000 | 0.002 | 0.504 | |
perimeter | at angle of Louis level [cm] | 87.3 (10.8) | 72.3 (16.3) | 85.8 (14.2) | 0.031 | 0.676 | 0.080 |
at xiphoid level [cm] | 87 (10.6) | 82.1 (24.1) | 93.1 (28.8) | 0.739 | 0.194 | 0.258 | |
at umbilical level [cm] | 82.1 (14.5) | 85.2 (24.5) | 94.5 (34.2) | 0.339 | 0.095 | 0.537 | |
area | chest wall [cm 2 ] | 4168 (979) | 2514 (1488) | 3826 (1652) | 0.002 | 0.378 | 0.016 |
at angle of Louis level [cm 2 ] | 527 (149) | 390 (182) | 524 (159) | 0.038 | 0.745 | 0.100 | |
at xiphoid level [cm 2 ] | 576 (145) | 507 (354) | 657 (407) | 0.868 | 0.137 | 0.258 | |
at umbilical level [cm 2 ] | 508 (197) | 560 (351) | 678 (511) | 0.406 | 0.078 | 0.440 | |
ratio | chest wall area/ chest wall volume [cm − 1 ] | 0.21 (0.03) | 0.25 (0.06) | 0.21 (0.04) | 0.009 | 0.781 | 0.014 |
trunk height/perimeter at xiphoid level | 0.46 (0.05) | 0.28 (0.06) | 0.31 (0.1) | 0.000 | 0.000 | 0.057 |