From: Lung and chest wall volume during vital capacity manoeuvre in Osteogenesis Imperfecta
 | OI Type III | OI Type I-IV |  | ||||
---|---|---|---|---|---|---|---|
 | median | 1st Q | 3rd Q | median | 1st Q | 3rd Q | p-value |
Age (years) | 37.0 | 32.7 | 45.8 | 33.3 | 17.2 | 44.5 | 0.409 |
Weight (kg) | 34.6 | 27.55 | 46.2 | 58.0 | 46.8 | 66.2 | < 0.001 |
Height (m) | 1.03 | 0.99 | 1.15 | 1.39 | 1.33 | 1.45 | < 0.001 |
BMI (kg/m 2 ) | 30.3 | 25.4 | 34.0 | 30.9 | 24.8 | 36.9 | 0.564 |
Thoracic scoliosis (Cobb angle) | 30.0 | 30.0 | 40.0 | 30.0 | 20.0 | 30.0 | 0.083 |
Lumbar scoliosis (Cobb angle) | 30.0 | 30.0 | 40.0 | 20.0 | 20.0 | 30.0 | 0.018 |
FVC (L) | 0.92 | 0.68 | 1.33 | 2.23 | 2.11 | 2.55 | <0.001 |
FVC (% predicted) | 66.4 | 46.1 | 79.6 | 82.3 | 74.6 | 90.8 | 0.059 |
FEV 1 (L) | 0.73 | 0.51 | 1.09 | 1.88 | 1.60 | 2.44 | <0.001 |
FEV 1 (% predicted) | 66.0 | 40.9 | 80.9 | 79.6 | 69.2 | 95.0 | 0.026 |
FEV 1 /FVCÂ (%) | 77.9 | 72.7 | 86.8 | 84.7 | 80.5 | 86.2 | 0.436 |
TLC (L) | 1.43 | 1.12 | 2.12 | 3.05 | 2.55 | 3.28 | < 0.001 |
TLC (% predicted) | 69.3 | 59.0 | 85.6 | 78.6 | 72.9 | 90.1 | 0.236 |
PEF (L/min) | 180 | 150 | 250 | 290 | 270 | 300 | 0.002 |
PCF (L/min) | 250 | 190 | 370 | 445 | 375 | 465 | 0.004 |
AHI (events/hour) | 10.0 | 4.0 | 17.4 | 2.3 | 1.0 | 6.7 | 0.012 |
ODI (events/hour) | 10.3 | 4.2 | 18.6 | 3.3 | 1.1 | 7.0 | 0.017 |
mean nocturnal SaO 2 (%) | 93.2 | 91.0 | 94.2 | 95.2 | 93.5 | 95.6 | 0.006 |