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Table 5 Hand function scores

From: A prospective short-term study to evaluate methodologies for the assessment of disease extent, impact, and wound evolution in patients with dystrophic epidermolysis bullosa

Disease severity Grade 0 (no fusion) Grade 1 (fusion extending to the proximal interphalangeal joint) Grade 2 (fusion extending to the distal interphalangeal joint of the longer finger) Grade 3 (fusion extending to the tip of the digit)
Right hand Left hand Right hand Left hand Right hand Left hand Right hand Left hand
 Mild
 N = 9
        
  Baseline 9 (100) 9 (100) 0 0 0 0 0 0
  Week 4 9 (100) 9 (100) 0 0 0 0 0 0
 Moderate
 N = 10
        
  Baseline 5 (50.0) 5 (50.0) 3 (30.0) 3 (30.0) 0 0 2 (20.0) 2 (20.0)
  Week 4 5 (50.0) 5 (50.0) 2 (20.0) 2 (20.0) 0 0 2 (20.0) 2 (20.0)
 Severe
 N = 11
        
  Baseline 2 (18.2) 2 (18.2) 3 (27.3) 5 (45.5) 1 (9.1) 0 5 (45.5) 4 (36.4)
  Week 4 2 (18.2) 2 (18.2) 3 (27.3) 5 (45.5) 0 0 6 (54.5) 4 (36.4)
Overall
N = 30
        
 Baseline 16 (53.3) 16 (26.7) 6 (20.0) 8 (26.7) 1 (3.3) 0 7 (23.3) 6 (20.0)
 Week 4 16 (53.3) 16 (26.7) 5 (16.7) 7 (23.3) 0 0 8 (26.7) 6 (20.0)