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Table 5 Hand function scores

From: A prospective short-term study to evaluate methodologies for the assessment of disease extent, impact, and wound evolution in patients with dystrophic epidermolysis bullosa

Disease severity

Grade 0 (no fusion)

Grade 1 (fusion extending to the proximal interphalangeal joint)

Grade 2 (fusion extending to the distal interphalangeal joint of the longer finger)

Grade 3 (fusion extending to the tip of the digit)

Right hand

Left hand

Right hand

Left hand

Right hand

Left hand

Right hand

Left hand

 Mild

 N = 9

        

  Baseline

9 (100)

9 (100)

0

0

0

0

0

0

  Week 4

9 (100)

9 (100)

0

0

0

0

0

0

 Moderate

 N = 10

        

  Baseline

5 (50.0)

5 (50.0)

3 (30.0)

3 (30.0)

0

0

2 (20.0)

2 (20.0)

  Week 4

5 (50.0)

5 (50.0)

2 (20.0)

2 (20.0)

0

0

2 (20.0)

2 (20.0)

 Severe

 N = 11

        

  Baseline

2 (18.2)

2 (18.2)

3 (27.3)

5 (45.5)

1 (9.1)

0

5 (45.5)

4 (36.4)

  Week 4

2 (18.2)

2 (18.2)

3 (27.3)

5 (45.5)

0

0

6 (54.5)

4 (36.4)

Overall

N = 30

        

 Baseline

16 (53.3)

16 (26.7)

6 (20.0)

8 (26.7)

1 (3.3)

0

7 (23.3)

6 (20.0)

 Week 4

16 (53.3)

16 (26.7)

5 (16.7)

7 (23.3)

0

0

8 (26.7)

6 (20.0)