Table 2 Characteristics of deceased individuals with alpha-mannosidosis reported by clinicians/PO and the literature, for which cause of death was available
From: Mortality in patients with alpha-mannosidosis: a review of patients’ data and the literature
Deceased individuals reported by | ||||||||
|---|---|---|---|---|---|---|---|---|
Clinicians/PO | Literature | |||||||
Male | Female | Unknown | Total | Male | Female | Unknown | Total | |
n (%) | 6 (40.0) | 8 (53.3) | 1 (6.7) | 15 | 4 (57.1) | 2 (28.6) | 1 (14.3) | 7 |
Age at death (years) | ||||||||
Median | 47.0 | 43.5 | 18 | 45.0 | 28.0 | 3.25 | 2.2 | 4.3 |
Mean ± SD | 44.8 ± 6.6 | 39.6 ± 15.1 | 18 | 40.3 ± 13.2 | 25.3 ± 17 | 3.25 ± 0.4 | 2.2 | 15.7 ± 17.0 |
Range | 35 − 52 | 20 − 56 | – | 18 − 56 | 4.3 − 41 | 3 − 3.5 | – | 2.2 − 41 |
Age at death, n (%) | ||||||||
0–9 | – | – | – | – | 1 (25) | 2 (100.0) | 1 (100) | 4 (57.1) |
10–19 | – | – | 1 (100) | 1 (6.7) | 1 (25) | – | – | 1 (14.3) |
20–29 | – | 3 (37.5) | – | 3 (20.0) | – | – | – | – |
30–39 | 2 (33.3) | 1 (12.5) | – | 3 (20.0) | 1 (25) | – | – | 1 (14.3) |
40–49 | 2 (33.3) | 1 (12.5) | – | 4 (26.7) | 1 (25) | – | – | 1 (14.3) |
≥ 50 | 1 (16.7) | 3 (37.5) | – | 4 (26.7) | – | – | – | – |