Fig. 1From: Characterization of hearing-impairment in Generalized Arterial Calcification of Infancy (GACI)Carhart notch example. Pure-tone audiogram from the right ear of a 25-year-old man with GACI showing a conductive hearing loss with narrowing of the air–bone gap at 2000 Hz characteristic of a Carhart notch. This patient’s tympanogram is normal (Type A) and acoustic stapedial reflexes are absentBack to article page