Characteristica | All patients (n = 127) | Pancreato-hepato-biliary (n = 59) | RPF/Aorta (n = 6) | Head and neck-limited (n = 15) | Mikulicz and systemic (n = 47) | P value |
---|---|---|---|---|---|---|
Male gender, n (%) | 92 (72.4%) | 47 (79.7%) | 6 (100%) | 7 (46.7%) | 32 (68.1%) | 0.03 |
Age at onset (years) | 63 (55–69) | 64.0 (55.0–69.0) | 61.0 (55.8–65.5) | 62.0 (54.0–72.0) | 63.0 (56.0–70.0) | 0.9 |
WBC (109/L) | 5.7 (4.5–7.1) | 5.5 (4.5–6.9) | 9.6 (6.6–11.0) | 6.1 (4.6–7.4) | 5.5 (4.2–7.3) | 0.02 |
Eosinophils (%) | 4.4 (2.1–7.5) | 4.5 (2.0–7.6) | 3.3 (1.8–4.3) | 4.3 (1.7–8.3) | 4.5 (2.6–7.7) | 0.7 |
ALT (U/L) | 33.5 (15.0–134.8) | 90 (32.0–175.0) | 17.0 (12.8–35.3) | 17 (14.0–24.5) | 20.0 (12.8–83.3) | 0.00 |
AST (U/L) | 31.9 (19.8–91.3) | 71.4 (26.0–130.5) | 16.8 (15.3–22.2) | 21.6 (18.8–25.7) | 25.0 (18.3–81.5) | 0.00 |
ALP (U/L) | 102 (22.0–525.0) | 316.5 (159.5–555.8) | 98.0 (78.5–103.0) | 76.0 (66.5–93.0) | 79.0 (66.0–283.5) | 0.00 |
GGT (U/L) | 140.0 (74.0–392.0) | 373.0 (70.0–817.0) | 45.5 (32.3–88.8) | 23.0 (17.0–31.0) | 32.0 (15.0–236.0) | 0.00 |
TBIL (umol/L) | 35.9 (32.3–39.0) | 53.9 (15.9–148.1) | 9.8 (8.5–12.3) | 10.8 (8.4–13.1) | 14.5 (9.8–32.2) | 0.00 |
DBIL (umol/L) | 34.2 (30.3–40.6) | 27.0 (4.4–98.0) | 1.9 (1.5–2.7) | 1.8 (1.5–2.3) | 3.3 (1.9–12.9) | 0.00 |
ALB (g/L) | 18.2 (10.8–70.6) | 35.5 (32.2–38.4) | 38.2 (35.4–41.5) | 38.6 (36.8–41.0) | 35.7 (30.5–39.2) | 0.03 |
GLO (g/L) | 5.5 (2.1–37.0) | 32.2 (29.5–37.7) | 34.1 (29.7–40.0) | 32.6 (30.0–42.8) | 37.0 (32.3–48.6) | 0.01 |
Cr (umol/L) | 69.7 (58.1–84.2) | 69.2 (54.8–77.5) | 110.1 (79.8–140.1) | 74.4 (62.5–91.0) | 69.0 (56.8–89.5) | 0.01 |
IgG (g/L) | 1775 (1527–2357) | 1680.0 (1475.0–2065.0) | 1540 (1315.0–1870.0) | 1545.0 (1240.0–2227.5) | 2020.0 (1680.0–2850.0) | 0.01 |
IgG4 (g/L) | 9.8 (3.9–15.2) | 10.3 (0.54–53.7) | 3.0 (1.7–6.8) | 8.2 (3.9–20.6) | 13.0 (4.5–22.1) | 0.01 |
IgG4-RD RI | 8.0 (6.0–10.0) | 6.0 (6.0–8.0) | 10.0 (8.0–17.0) | 6.0 (4.0–8.0) | 10.0 (6.0–14.0) | 0.00 |