Table 1 Baseline characteristics of patients with and without severe ADAMTS13 deficiency
From: Lombardy diagnostic and therapeutic network of thrombotic microangiopathy
ADAMTS13 < 10% (n = 35) | ADAMTS13 ≥ 10% (n = 8) | Difference of proportions/ median difference (95% CI) | |
|---|---|---|---|
Female sex, n (%) | 23 (66) | 3 (38) | 28 (− 17–73) |
Age at 1st episode, median (IQR) | 48 (29–60) | 58 (50–79) | − 18 (− 31 to − 1) |
Age at enrollment, median (IQR) | 50 (40–63) | 58 (50–79) | − 13 (− 28–3) |
BMI, kg/m2, median (IQR) | 25 (22–28)a | 25 (23–26) | 0.87 (− 2.56–4.57) |
Autoimmune disease, n (%) | 11 (31) | 1 (13) | 18 (− 16–54) |
Cancer, n (%) | 0 (0) | 4 (50) | − 50 (− 92 to − 8) |