Table 2 Clinical and biochemical characteristics of episodes at admission
Children (N = 39) | Adults (N = 87) | All (N = 126) | |
|---|---|---|---|
Age categories at admission | |||
1–10 years | 17 (43.6%) | 0 | 17 (13.5%) |
11–15 years | 14 (35.9%) | 0 | 14 (11.1%) |
≥ 15 years | 0 (0.0%) | 87 (100.0%) | 87 (69.0%) |
Number of patients/Range of number of episodes per patient | 13/1–11 | 11/1–30 | 24/1–30 |
Main precipitating factors | |||
Infectious episodes | 16 (41.0%) | 25 (28.7%) | 41 (32.5%) |
Dietary non-adherence | 7 (17.9%) | 30 (34.5%) | 37 (29.4%) |
Neonatal/first diagnosis | 2 (5.1%) | 0 (0.0%) | 2 (1.6%) |
Vaccination | 0 (0.0%) | 2 (2.3%) | 2 (1.6%) |
Stress | 0 (0.0%) | 2 (2.3%) | 2 (1.6%) |
Other (no detail) | 2 (5.1%) | 17 (19.5%) | 19 (15.1%) |
Missing | 12 (30.7%) | 11 (12.6%) | 23 (18.3%) |
Leucine plasma concentration at admission | |||
< 381 µmol/L (< 5 mg/100 mL) | 6 (15.4%) | 2 (2.3%) | 8 (6.3%) |
381–762 µmol/L (5–10 mg/100 mL) | 8 (20.5%) | 13 (14.9%) | 21 (16.7%) |
> 762 µmol/L (10 mg/100 mL) | 22 (56.4%) | 70 (80.5%) | 92 (73.0%) |
Missing | 3 (7.7%) | 2 (2.3%) | 5 (4.0%) |