Skip to main content

Table 3 Extraocular manifestations and findings

From: Various vascular malformations are prevalent in Finnish pseudoxanthoma elasticum (PXE) patients: a national registry study

Variable

n/mean

%/range

Skin biopsy

13

69.9

 Positive

12

57.1

Cerebrovascular arterial disease

5

23.8

Patients with vascular malformations

4

19.0

 Individual malformations

5

 

Intra-abdominal hemorrhagic event

6

28.6

Nephrolithiasis

4

19.0

Peripheral artery disease

6

28.6

 Claudication

5

23.8

 Critical limb ischemia

2

9.5

Ankle-brachial index measured

8

38.1

 Abnormal results

5

23.8

Mean abnormal ABI (right/left)

0.64/0.56

0.38–0.77/0.40–0.78

  1. ABI ankle-brachial index