Fig. 4

Digital subtraction angiography of a patient’s cerebral arteries. Only a stump of the right internal carotid artery can be visualized (arrow). The patient’s left eye was blind at birth and in a subsequent investigation loss of vision was postulated to have occurred due to a steal effect on the ophthalmic artery, caused by a bilateral carotid artery dissection. The patient was thought to have survived due to extensive anastomosing of carotid and cerebral arteries. The dissected portion of the left carotid artery is not visible. Retrospectively we hypothesize this to be a manifestation of either generalized arterial calcification in infancy type 2, or internal carotid artery hypoplasia