Therapeutic potential of living donor liver transplantation from heterozygous carrier donors in children with propionic acidemia

Table 2 Pretransplant and posttransplant clinical index of patients with propionic acidemia

	Follow-up time, months	Outcome	Current age, years	Metabolism correcting medication		Protein intake, g/kg/day		Support feeding		Metabolic decompensations		Cardiomyopathy		DQ
	Follow-up time, months	Outcome	Current age, years	Pre	Post	Pre	Post	Pre	Post	Pre	Post	Pre	Post	Pre	Post
1	40.2	Alive	5.0	Levocarnitine	Levocarnitine	N/A	Normal diet	N	N	Y	N	N	N	77	85
2	39.8	Alive	5.3	Levocarnitine	Levocarnitine	1.25	Normal diet	N	N	Y	N	N	N	69	74
3	37.5	Alive	8.9	Levocarnitine Sodium bicarbonate	Levocarnitine	2.5	Normal diet	N	N	Y	N	N	N	54	57
4	23.9	Alive	3.2	Levocarnitine	Levocarnitine	0.8	Normal diet	N	N	Y	N	N	N	37	45
5	21.6	Alive	4.5	Levocarnitine Sodium benzoate Sodium bicarbonate	Levocarnitine	2.25	Normal diet	N	N	Y	N	Y	N	86	90
6	18.6	Alive	6.1	Levocarnitine	Levocarnitine	2.7	Normal diet	N	N	Y	N	N	N	92	94
7	13.9	Alive	2.3	Levocarnitine	Levocarnitine	1.0	Normal diet	N	N	Y	N	N	N	78	78

ISSN: 1750-1172