Item | Type | Number | α-Genotype | Hb Bart’s (%) |
---|---|---|---|---|
1 | Non α-thalassemia | 152 | αα/αα | 0 |
2 | Hb Bart’s Hydrops fetalis | 57 | --/-- | 81.5 ± 3.6 (74.7–89.9) |
3 | α0-thalassemia trait | 44 | --/αα | 4.8 ± 1.2 (1.9–8.0) |
4 | α+-thalassemia trait | 26 | -α/αα | 0.7 ± 0.4 (0–1.5) |
5 | Homozygous Hb CS and Hb CS/Hb PS | 14 | αCSα/αCSα (11), αCSα/αPSα (3) | 11.2 ± 2.6 (7.4–16.7) |
6 | Hb CS trait | 12 | αCSα/αα | 1.3 ± 0.8 (0.4–2.9) |
7 | Hb H disease | 7 | --/-α | 19.2 ± 1.5 (16.9–22.1) |
8 | Hb H-CS and Hb H-Pakse’ diseases | 6 | --/αCSα (5), --/αPSα (1) | 26.3 ± 1.8 (23.4–28.2) |
9 | α+-thalassemia/Hb CS | 5 | αCSα/- α | 7.3 ± 2.2 (4.8–9.9) |
10 | Homozygous α+-thalassemia | 4 | -α/-α | 4.1 ± 1.5 (2.1–5.8) |
11 | Rare α+-thalassemia trait | 2 | ααQP/αα | 0.5 |
ααAms/αα | 0.5 | |||
12 | Hb H-QZ disease | 1 | --/αQZα | 33.7 |
13 | Unknown | 2 | na | 0.7, 1.4 |
Total | 332 |