Epidermolysis Bullosa in children: the central role of the pediatrician

Table 7 Frequency of blood exams and investigations in patients with severe EB major types

Investigations	0–1 y patients	1–10 y patients	10–20 y patients	>20 y patients
Blood exams¹	6–12 months²	12 months	12 months	12 months
Hormonal assessment	–	–	12 months	12 months
Specialist evaluation³	6–12 months	6–12 months	6–12 months	6–12 months
Psychological evaluation	6–12 months (parents)	6–12 months (Parents and child)	6–12 months (Parents and child)	6–12 months (Parents and child)
Imaging examinations⁴	12 months	12 months	12 months	12 months
Dual X-ray	–	–	12 months	12 months

Vaccinations should be performed for all EB patients independently on age and EB types, according with Vaccination Action Plan
¹Complete blood cell count, hemoglobin, mean cellular volume, reticulocytes, ferritin, serum iron, CRP, ESR, renal function, electrolytes, immunoglobulin, total protein, albumin, zinc, selenium, vitamin D, B6, folate, vitamin B12, carnitine
²To be anticipated in case of acute signs or symptoms of the disease manifesting before the given age
³Dentist, pain therapist, physiotherapist, endocrinologist, endoscopist, hematologist, nutritional experts, ophthalmologist, cardiologist in addition to pediatricians and dermatologists.
⁴Orthopantomograph

ISSN: 1750-1172