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Table 2 VOC prevalence distribution studies

From: A systematic literature review of frequency of vaso-occlusive crises in sickle cell disease

Study identifier

Country

N

Mean age

VOC definition

Distribution of VOC, %

Adekile et al. [ 53]

Kuwait

396

19.2

Hospitalization

0/year: 3.3

     

1/year: 54.8

     

2–3/year: 13.2

     

> 3/year: 18.9

Aloni et al. [54]

Democratic Republic of Congo

168

10

Hospitalization > 48 h

0/year: 3.6

     

1–3/year: 51.8

     

> 3/year: 44.6

Andemariam et al. [20]

U.S

384

30.1

Self-reported (patient survey; hospitalization, ED, managed at home)

0/year: 4

     

1–4/year: 38

     

≥ 5/year: 59

Bailey et al. [14]

England

15,076

30a

Healthcare visit (OP, IP, or ED)

≥ 3/year: 4

Dave et al. [47]

India

404

19

Healthcare visit (OP or IP) to care system

0/year: 11.9

     

1/year: 15.6

     

2/year: 22.8

     

≥ 3/year: 49.8

Delicou et al. [23]

Greece

254

NR

Healthcare visit (OP, IP, or ED)

0/year: 25.3

     

1–5/year: 50.6

     

5–10/year: 8.3

     

> 10/year: 15.8

James et al. [19]

Multiple

1513

24.1

Self-reported (patient survey; hospitalization, ED, managed at home)

0/year: 8

     

1–4/year: 51

     

≥ 5/year: 40

Latremouille-Viau et al. [49]

U.S

18,287b

28.5

Healthcare visit (OP, IP, or ED); Medicaid and Medicare claims

0/year: 36.1

     

1/year: 17

     

≥ 2/year: 46.8

  

15,431c

48.2

 

0/year: 44.9

     

1/year: 11.4

     

≥ 2/year: 43.7

Rizio et al. [13]

U.S

303

34.4

Self-reported (ASCQ-Me)

0/year: 8.9

     

1/year: 9.6

     

2/year: 14.5

     

3/year: 19.8

     

≥ 4/year: 47.2

Shah et al. [22]

U.S

8521

32.9

Healthcare visit (OP, IP, or ED); Medicaid claims

0/year: 52.3

     

1/year: 14.7

     

2/year: 6.7

     

3/year: 4.6

     

4/year: 3.7

     

5/year: 2.7

     

6/year: 2

     

7/year: 1.5

     

8/year: 1.4

     

9/year: 1.4

     

> 10/year: 9.2

van Tuijn et al. [55]

Netherlands

95

37a

Hospitalization

0/year: 23

     

0–1/year: 43

     

> 1/year: 16

  1. ASCQ-Me adult sickle cell quality of life measurement information system, ED emergency department, IP inpatient, NR not reported, OP outpatient, VOC vaso-occlusive crisis
  2. aMedian reported
  3. bMedicaid claims study arm
  4. cMedicare claims study arm