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Table 2 Hearing loss in adults with achondroplasia, by age groups

From: Hearing loss in Norwegian adults with achondroplasia

Age groups, years All 16–44 y 45–64 y > 64 y
(N = 45) (n = 28) (n = 14) (n = 3)
N (%) N (%) N (%) N (%)
Hearing loss in at least one eara     
 Mild (20–34 dB) 18 (40) 12 (43) 6 (43) 0 (0)
 Disabling (≥ 35 dB) 6 (13) 2 (7) 1 (7) 3 (100)
Unilateral hearing lossa     
 Mild (20–34 dB) 3 (7) 3 (11) 0 (0) (0)
 Disabling (≥ 35 dB) 2 (4) 2 (8) 0 (0) (0)
Hearing loss in the better earb     
 Mild (20–34 dB) 15 (33) 9 (32) 6 (43) 0 (0)
 Disabling (≥ 35 dB) 4 (9) 0 (0) 1 (7) 3 (100)
Abnormal tympanometryc     
 Unilateral 8 (18) 5 (18) 3 (21) 0 (0)
 Bilateral 24 (53) 12 (43) 9 (64) 3 (100)
Abnormal stapedius reflexd     
 Unilateral 5 (11) 3 (11) 2 (14) 0 (0)
 Bilateral 27 (60) 16 (57) 8 (57) 3 (100)
Type of hearing loss     
 Conductive 15 (33) 12 (43) 3 (21) 0 (0)
 Sensorineural 1 (2) 1 (4) 0 (0) 0 (0)
 Mixed 8 (18) 1 (4) 4 (29) 3 (100)
  1. dB decibel
  2. aBased on PTA over 0.25, 0.5, 1, 2, 4, 6 and 8 kHz
  3. bBased on PTA over 0.5, 1, 2 and 4 kHz (BE PTA4)
  4. cDefined as Type B or C
  5. dAbsent or reduced contraction of the stapedius muscles