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Table 2 Hearing loss in adults with achondroplasia, by age groups

From: Hearing loss in Norwegian adults with achondroplasia

Age groups, years

All

16–44 y

45–64 y

> 64 y

(N = 45)

(n = 28)

(n = 14)

(n = 3)

N (%)

N (%)

N (%)

N (%)

Hearing loss in at least one eara

    

 Mild (20–34 dB)

18 (40)

12 (43)

6 (43)

0 (0)

 Disabling (≥ 35 dB)

6 (13)

2 (7)

1 (7)

3 (100)

Unilateral hearing lossa

    

 Mild (20–34 dB)

3 (7)

3 (11)

0 (0)

(0)

 Disabling (≥ 35 dB)

2 (4)

2 (8)

0 (0)

(0)

Hearing loss in the better earb

    

 Mild (20–34 dB)

15 (33)

9 (32)

6 (43)

0 (0)

 Disabling (≥ 35 dB)

4 (9)

0 (0)

1 (7)

3 (100)

Abnormal tympanometryc

    

 Unilateral

8 (18)

5 (18)

3 (21)

0 (0)

 Bilateral

24 (53)

12 (43)

9 (64)

3 (100)

Abnormal stapedius reflexd

    

 Unilateral

5 (11)

3 (11)

2 (14)

0 (0)

 Bilateral

27 (60)

16 (57)

8 (57)

3 (100)

Type of hearing loss

    

 Conductive

15 (33)

12 (43)

3 (21)

0 (0)

 Sensorineural

1 (2)

1 (4)

0 (0)

0 (0)

 Mixed

8 (18)

1 (4)

4 (29)

3 (100)

  1. dB decibel
  2. aBased on PTA over 0.25, 0.5, 1, 2, 4, 6 and 8 kHz
  3. bBased on PTA over 0.5, 1, 2 and 4 kHz (BE PTA4)
  4. cDefined as Type B or C
  5. dAbsent or reduced contraction of the stapedius muscles