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Table 2 Dignostic criteria for congenital hyperinsulinism

From: Genetic pathogenesis, diagnosis, and treatment of short-chain 3-hydroxyacyl-coenzyme A dehydrogenase hyperinsulinism

  Detected when plasma glucose < 2.8 mmol/L
Plasma insulin, plasma C-peptide  > 1–2uU/mL (insulin), > 0.2 mmol/L (C-peptide)
Plasma free fatty acids  < 1.7 mmol/L
Plasma β-hydroxybutyrate  < 1.8 mmol/L
Glycemic response to glucagon  ≥ 1.7 mmol/L