Patient number | Time on ERT, years | FVC (mL) | FEV1 (mL) | 6MWT (m) | |||
---|---|---|---|---|---|---|---|
Before ERT | Last visit | Before ERT | Last visit | Before ERT | Last visit | ||
1 | 1 | 1663 | 1610 | 1361 | 1358 | 125 | 150 |
2 | 1 | 1430 | 1452 | 1148 | 1154 | 39 | 86.4 |
3 | 6 | 938 | 1318 | 896 | 1068 | 32 | 424 |
4 | 4 | 2460 | 2690 | 2180 | 2360 | – | – |
5 | 4 | 780 | 870 | 680 | 730 | 302 | 351 |