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Table 1 Characteristics of the study population (n = 35)

From: Functional mobility in walking adult population with ataxia of Charlevoix-Saguenay

Characteristic

Total group

n = 35

No walking aid

n = 19

Walking aid

n = 16

p-value*

Age, (y)

Mean (SD)

32.2 (10.4)

26.5 (7.6)

38.9 (9.4)

< 0.001

Range

16–65

16–42

25–65

 

Sex, n (%)

Men

15 (42.9)

11 (73.3)

4 (26.7)

0.087

Women

20 (57.1)

8 (40.0)

12 (60.0)

Age groups, n (%)

16–29

14 (40.0)

13 (92.9)

1 (7.1)

 

30–39

16 (45.7)

5 (11.0)

11 (68.8)

≥ 40

5 (14.3)

1 (20.0)

4 (80.0)

 

Falls (period)

6 months

 Mean (SD)

8.8 (11.1)

11.1 (13.5)

6.3 (7.3)

0.219

 Range

0–50

0–50

0–26

 

1 year

 Mean (SD)

17.6 (22.1)

21.6 (26.9)

13.0 (14.4)

0.262

 Range

0–100

0–100

0–52

 

Disease severity

DSI-ARSACS (/38)

 Mean (SD)

13.5 (4.3)

10.8

16.7

< 0.001

 Range

4.5–22.0

4.5–16.0

11.0–22.0

 

SARA (/40)

 Mean (SD)

13.4 (5.9)

9.2 (4.0)

18.5 (3.0)

< 0.001

 Range

4.0–22.5

4.0–20.0

11.0–22.5

 
  1. *Statistical difference between mobility stages
  2. Bold indicates p value < 0.05