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Table 3 Secondary outcome results

From: Long-term effectiveness of carglumic acid in patients with propionic acidemia (PA) and methylmalonic acidemia (MMA): a randomized clinical trial

Biomarker

Relative change

95% LCL

95% UCL

p-value

Ammonia: Carglumic acid versus standard

0.868924

0.725061

1.041435

0.1283

Glycine: Carglumic acid versus standard

0.748039

0.561861

0.995809

0.0468

Methionine: Carglumic acid versus standard

1.004108

0.861483

1.17023

0.9585

Leucine: Carglumic acid versus standard

0.89682

0.720219

1.116836

0.3306

Isoleucine: Carglumic acid versus standard

0.952276

0.680859

1.331891

0.7753

Valine: Carglumic acid versus standard

0.918972

0.753746

1.120416

0.4035

Threonine Carglumic acid versus standard

1.02429

0.781219

1.342992

0.8623

Glutamine Carglumic acid versus standard

0.965316

0.820534

1.135644

0.6704