| Overall | Standard therapy N = 17 | Carglumic acid N = 16 |
---|---|---|---|
Mean total ER visits (STD) | 9.64 ± 9.12 | 12.76 ± 11.18 | 6.31 ± 4.61 |
Min | 0.00 | 0.00 | 0.00 |
Max | 41.00 | 41.00 | 16.00 |
Total ER visits | |||
 0 visits n (%) | 5 (15.15)% | 3 (17.65%) | 2 (12.50%) |
 1–2 visits n (%) | 3 (9.09)% | 1 (5.88%) | 2 (12.50%) |
 3–4 visits n (%) | 4 (12.12)% | 2 (11.76%) | 2 (12.50%) |
 5–6 visits n (%) | 4 (12.12)% | 1 (5.88%) | 3 (18.75%) |
 More than 6 Visits n (%) | 17 (51.52)% | 10 (58.82%) | 7 (43.75%) |