Table 5 Kidney transplant cohort and main disease categories leading to transplantation
From: The frequency of rare and monogenic diseases in pediatric organ transplant recipients in Italy
Disease macro-category | Pediatrics (n. 887) | Adults (n. 18,553) | Total (n. 19,440) |
|---|---|---|---|
n. (%) | n. (%) | n. (%) | |
Congenital familial rare and metabolic based nephro- and uro-pathies | 670 (75.5) | 378 (2.0) | 721 (3.7) |
Glomerular nephropathies | 89 (10.0) | 7,438 (40.1) | 7,527 (38.7) |
Cystic nephropathies | 43 (4.8) | 3,493 (18.8) | 3,536 (18.2) |
Acute renal insufficiency | 13 (1.5) | 43 (0.2) | 56 (0.3) |
Other familial nephropathies | 12 (1.4) | 227 (1.2) | 239 (1.2) |
Different nephro-vasculopathic and nephrosclerosis syndromes | 7 (0.8) | 389 (2.1) | 396 (2.0) |
Kidney neoplasia | 2 (0.2) | 53 (0.3) | 55 (0.3) |
Hypertensive nephrosclerosis | 1 (0.2) | 1,610 (8.7) | 1,611 (8.3) |
Tubular and interstitial nephropathies | 0 (0.0) | 1,326 (7.1) | 1,326 (6.8) |
Diabetic nephropathy | 0 (0.0) | 1,409 (7.6) | 1,409 (7.2) |
Non-cholestatic cirrhosis | 0 (0.0) | 2 (0.0) | 2 (0.0) |
Other hepatopathies | 3 (0.3) | 1 (0.0) | 4 (0.0) |
Other kidney disorders | 47 (5.3) | 2,184 (11.8) | 2,558 (13.2) |