From: The frequency of rare and monogenic diseases in pediatric organ transplant recipients in Italy
Disease macro-category | Pediatrics (n. 1,037) | Adults (n. 15,836) | Total (n. 16,873) |
---|---|---|---|
n. (%) | n. (%) | n. (%) | |
Hepatopathies from atresia of the biliary tract | 433 (41.8) | 32 (0.2) | 465 (2.8) |
Metabolic diseases | 126 (12.2) | 350 (2.2) | 476 (2.8) |
Cholestatic cirrhosis and other cholestatic liver diseases | 121 (11.7) | 857 (5.4) | 978 (5.8) |
Neoplasia | 83 (8.0) | 4,505 (28.4) | 4,588 (27.2) |
Acute liver necrosis | 44 (4.2) | 404 (2.6) | 448 (2.7) |
Other non-cholestatic cirrhosis | 43 (4.1) | 5,950 (37.6) | 5,993 (35.5) |
HBV/HCV related cirrhosis | 5 (0.5) | 1,116 (7.0) | 1,121 (6.6) |
Alcoholic cirrhosis | 0 (0.0) | 1,686 (10.6) | 1,686 (10.0) |
Other hepatopathies | 182 (17.5) | 936 (5.9) | 1,118 (6.6) |