Characteristic | Proportion with mRS 3 +  | Median (range) |
---|---|---|
Mutation | ||
 ACVRL1 | 18/475 (4%) | 1 (0–5) |
 Endoglin | 31/619 (5%) | 1 (0–4) |
SMAD4 | 3/39 (8%) | 1 (0–4) |
Brain VM | 28/342 (8%) | 1 (0–5) |
Pulmonary AVM | 51/788 (6%) | 1 (0–5) |
Liver VM | 28/267 (10%) | 1 (0–5) |
GI bleeding | 34/264 (13%) | 1 (0 –5) |
Anemia | 63/751 (8%) | 1 (0–5) |